EVANS SYNDROME QUESTIONNAIRE


     Although these questions were mostly geared to children as this has been the biggest focus of our research, anyone with Evans syndrome is welcomed to review the questions and answer any or all. Please feel free to add any other information you think may or may not be relevant. It is our belief that if we ask enough questions, gather enough data, and find any common denominators, we just might get some answers...You may print this questionnaire, complete it at your leisure and mail it to the Evans Syndrome Research and Support Group, 1376 Presidential Highway, Jefferson, NH 03583 Or, you may FAX it to us at (603)586-7983.

1.Physical characteristics

Size for age___________________________________________________________________________________

Hair color____________________________________________________________________________________

Eye color_____________________________________________________________________________________

Facial features---anything unusual?________________________________________________________________

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Nose--anything different? Pinched nostrils? Wide and flat bridge between the eyes?________________________

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Eyes--shape, size, any slanting? Describe:__________________________________________________________

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Jaw--is it small? Small or large mouth?_____________________________________________________________

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Tongue--short or long? Is it pointy?_______________________________________________________________

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Ears---any funny creases on earlobes? Anything different?____________________________________________

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Fingers and toes--are they long or short? Anything different?________________________________________

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Male or female, any early signs of puberty? Early breast development? Describe:_________________________

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***If you would like to send a photograph of your child (or you) that we can attach to the survey, please feel free to do so.***

2.Is your child right or left handed?___________________________________________________________

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3. Any history of genetic problems with your child or any close relative?
(Close relatives up to your child's first cousin) If so, what and who?

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Any cleft palates?____________________________________________________________________________

Any cleft lips?_______________________________________________________________________________

Any webbing of the fingers or toes? If so, where? Any deformities?___________________________________

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Any birth defects?____________________________________________________________________________

Any developmental delays? Learning disabilities?___________________________________________________

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Any other little thing you can think of?.__________________________________________________________

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4. Pregnancy--was it normal?____________________________________________________________

Any complications? If so, what?___________________________________________________________________________

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Any medications used during pregnancy? If so, what?______________________________________________________

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Were you exposed to anything that you know of at home or at work?____________________________________________

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How about your husband, what does he do for work? Was he exposed to anything? Is he on any medications?

____________________________________________________________________________________________

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Were either of you in Vietnam?___________________________________________________________________

Desert Storm?____________________________________________________________________________________

Were you on birth control pills prior to pregnancy? If so, for how long?______________________________________________

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Delivery--any complications?_________________________________________________________________

What drugs were used in labor and delivery?_______________________________________________________________

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Were you given any antibiotics?_______________________________________________________________

If yes, by mouth or by IV? Did the baby get any antibiotics, blood or drugs? What?_________________________________

Any problems at birth with the baby?___________________________________________________________________

____________________________________________________________________________________________

Any idea what the baby's Apgar scores were?__________________________________________________________

Umbilical cord--was it normal with 3 vessels as far as you know?_______________________________________

Any feeding problems with the baby?____________________________________________________________________

Did you breast feed?_________________________ If so, for how long?______________________________________

Any milk intolerance with the baby?___________If so, were they on a soy formula like prosobee?____________________

6. Any history of blood disorders or immune disorders in anyone else in your family?
Or, any other "strange" or "rare" diseases? If so, what and who had it?

____________________________________________________________________________________________

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7. Immunizations (please complete this part as fully as possible)

How many did they get so far?--Polio________DPT________DtaP_______MMR_______

Hemophilus Influenza_______Hepatitis_______Chicken Pox_______ Any others?_______

Any reactions? What kind and how soon after ?________________________________________________

____________________________________________________________________________________________

Any seizures after the shots?_______________________________________________________________

Any fever after the shots? How long after and how high?_____________________________________

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Any inconsolable crying or high pitched crying after immunization?__________________________

Did your child have any illnesses within a week of any immunizations?_________________________

If so, what kind? (flu, diarrhea, cold etc.)_________________________________________________

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How long after their last immunizations (or flu shots) before they were diagnosed with Evans syndrome?

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8. What led up to you or your child getting this diagnosis?_____________________________________

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Had they been sickly as an infant?__________________________________________________________

Did they have frequent ear infections?__________________________________________________________

Were they taking any antibiotics just before they were diagnosed with Evans syndrome? If so, what?

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Any swollen glands or lumps in their neck or underarms?______________________________________

Do you own any pets or animals?_______________________________________________________________

Had you noticed bruising or excessive bleeding from minor injuries before the diagnosis?
Nosebleeds? Bleeding gums? If so, for how long before?

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Were there any complaints of not feeling well prior to diagnosis? If so, for how long?

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How old were they when they were diagnosed?__________________________________________________

Have they developed normally as far as you can tell?_____________________________________________

How old were they when they first walked?______________________Talked?______________________

Any problems with teething?__________________________________________________________________

9. What kind of treatment has been tried?______________________________________________________

Spleen removed? If so, at what age, how long after diagnosis and how have they done since?

____________________________________________________________________________________________

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How often is blood work done?________________________________________________________________

Are they on steroids? Prednisone? How much and for how long?______________________________________

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Ever received IVIG (IGIV/immune globulin/gamma globulin)? If so, when was it given, only in crisis
or ever tried routinely? Any relief?

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Transfusions? When? What kind--platelets, red cells? Any problems?_______________________________

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Chemotherapy? What kind? What benefit did you have?_____________________________________________

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Cyclosporin?_______________Prayer?!_________________Anything else?________________________

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10. Other miscellaneous tidbits and questions...

Any food intolerance or reactions to certain food additives that you've noticed? (like yellow dye #5, or MSG etc.)

____________________________________________________________________________________________

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Do you have trouble with white blood cell counts dropping? Neutropenia?_____________________________

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Have they had measles or chicken pox? Whooping cough? If so, how did they do with it?

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Are they around other children very much? Siblings? Day care?___________________________________

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Do they go to regular school if they are of school age? How do they tolerate it?_______________________

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Do they have rashes that come and go?________________________________________________________

If they have rashes, please describe where they get them, and how they look.__________________________

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Do they complain of leg cramps, arm cramps or muscle aches?____________________________________

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Do they have normal endurance? Like, can they run and play and keep up with the other kids?

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Do they have allergies? What kind?_____________________________________________________________

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Are they sensitive to medications or perhaps the flavorings and dyes in them?
Do medications seem to make them hyper or jittery?

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Where do you live? City/state/near water treatment plant or power plant etc.___________________________

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Did you travel anywhere with the child either while pregnant or later, on a family vacation?_________________

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What race are you? Any specific ethnic origins? (American Indian or Italian etc.)_______________________

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Are they Coombs positive?__________Are they "ANA" negative?_________(lupus test)

Is there any specific time of year that seems to be more of a problem with blood levels?____________________

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Was a bone marrow biopsy done? What were the results?__________________________________________________

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11. Is there anything that concerns you about your child, now or in the past that you've wondered
about but never thought it was anything big enough to ask the doctor about?


____________________________________________________________________________________________

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12. Is there anything you have a feeling about with your child? Any sixth sense feelings?
NOTHING IS INSIGNIFICANT!


____________________________________________________________________________________________

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13. Has your child been seen by a geneticist? What did they say?_____________________________

____________________________________________________________________________________________

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Who did they see?_____________________________________________________________________________________

14. Do they have any problems with their bowels? Diarrhea or constipation?
Have you noticed problems with either when their counts are low?
____________________________________________________________________________________________

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15. If you know, what is the usual range of blood levels for your child? What would you say is a safe
level for them--for example, one that is lower than normal, but that they seem to tolerate well.


White blood cells___________________________________________________________________________________________

Red blood cells______________________________________________________________________________________________

Platelets____________________________________________________________________________________________________

Is there anything else you would like to add? Anything else you think we should ask?_________________________

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Your name:__________________________________________________________________________________________

Child's name:_______________________________________________________________________________________

Address:_______________________________________________________________________________________________

____________________________________________________________________________________________

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Telephone Number:__________________________________________________________________________________

E-mail Address:______________________________________________________________________________________________

May we use this information without any names or identifying data in any articles that may result from tabulating the information?

YES___________________NO__________________


Would you like your name and phone number placed on a list with other people with Evans syndrome to be distributed to all for open communication and support?

YES___________________NO__________________


Please sign below:


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Thank you for your time.

Lou Addington, Founder

1999 Evans Syndrome Research and Support Group

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